Molecular Chaperones as Targets to Circumvent the CFTR Defect in Cystic Fibrosis

Por Chanoux, Rebecca A., Rubenstein, Ronald C.
Publicado em 2012

On Preventing the Extinction of the Physician-Scientist in Pediatric Pulmonology

Por Rubenstein, Ronald C., Kreindler, James L.
Publicado em 2014

Patient and parent perceptions of the diagnosis and management of cystic fibrosis-related diabetes()

Por Millington, Kate, Miller, Victoria, Rubenstein, Ronald C., Kelly, Andrea
Publicado no J Clin Transl Endocrinol (2014)

Elevation of 1-Hour Plasma Glucose During Oral Glucose Tolerance Testing Is Associated With Worse Pulmonary Function in Cystic Fibrosis

Por Brodsky, Jill, Dougherty, Shayne, Makani, Ramkrishna, Rubenstein, Ronald C., Kelly, Andrea
Publicado em 2011

Body Composition and Pulmonary Function in Cystic Fibrosis

Por Sheikh, Saba, Zemel, Babette S., Stallings, Virginia A., Rubenstein, Ronald C., Kelly, Andrea
Publicado em 2014

ERp29 regulates epithelial sodium channel functional expression by promoting channel cleavage

Por Grumbach, Yael, Bikard, Yann, Suaud, Laurence, Chanoux, Rebecca A., Rubenstein, Ronald C.
Publicado em 2014

Hsc70 negatively regulates epithelial sodium channel trafficking at multiple sites in epithelial cells

Por Chanoux, Rebecca A., Shubin, Calla B., Robay, Amal, Suaud, Laurence, Rubenstein, Ronald C.
Publicado em 2013

Regulation of endogenous ENaC functional expression by CFTR and ΔF508-CFTR in airway epithelial cells

Por Rubenstein, Ronald C., Lockwood, Shannon R., Lide, Ellen, Bauer, Rebecca, Suaud, Laurence, Grumbach, Yael
Publicado em 2011

Hsp70 Promotes Epithelial Sodium Channel Functional Expression by Increasing Its Association with Coat Complex II and Its Exit from Endoplasmic Reticulum

Por Chanoux, Rebecca A., Robay, Amal, Shubin, Calla B., Kebler, Catherine, Suaud, Laurence, Rubenstein, Ronald C.
Publicado em 2012

Hsp70 promotes epithelial sodium channel functional expression by increasing its association with coat complex II and its exit from endoplasmic reticulum.

Por Chanoux, Rebecca A., Robay, Amal, Shubin, Calla B., Kebler, Catherine, Suaud, Laurence, Rubenstein, Ronald C.
Publicado em 2012

4-Phenylbutyrate Stimulates Hsp70 Expression through the Elp2 Component of Elongator and STAT-3 in Cystic Fibrosis Epithelial Cells

Por Suaud, Laurence, Miller, Katelyn, Panichelli, Ashley E., Randell, Rachel L., Marando, Catherine M., Rubenstein, Ronald C.
Publicado em 2011

Differential effects of Hsc70 and Hsp70 on the intracellular trafficking and functional expression of epithelial sodium channels

Por Goldfarb, Samuel B., Kashlan, Ossama B., Watkins, Jeffrey N., Suaud, Laurence, Yan, Wusheng, Kleyman, Thomas R., Rubenstein, Ronald C.
Publicado em 2006

IL-17A Induces Pendrin Expression and Chloride-Bicarbonate Exchange in Human Bronchial Epithelial Cells

Por Adams, Kelly M., Abraham, Valsamma, Spielman, Daniel, Kolls, Jay K., Rubenstein, Ronald C., Conner, Gregory E., Cohen, Noam A., Kreindler, James L.
Publicado em 2014

ERp29 Regulates ΔF508 and Wild-type Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Trafficking to the Plasma Membrane in Cystic Fibrosis (CF) and Non-CF Epithelial Cell...

Por Suaud, Laurence, Miller, Katelyn, Alvey, Lora, Yan, Wusheng, Robay, Amal, Kebler, Catherine, Kreindler, James L., Guttentag, Susan, Hubbard, Michael J., Rubenstein, Ronald C.
Publicado em 2011

Efficacy and safety of ivacaftor treatment: randomized trial in subjects with cystic fibrosis who have an R117H-CFTR mutation

Por Moss, Richard B., Flume, Patrick A., Elborn, J. Stuart, Cooke, Jon, Rowe, Steven M., McColley, Susanna A., Rubenstein, Ronald C., Higgins, Mark
Publicado no Lancet Respir Med (2015)

Cystic fibrosis transmembrane conductance regulator contributes to reacidification of alkalinized lysosomes in RPE cells

Por Liu, Ji, Lu, Wennan, Guha, Sonia, Baltazar, Gabriel C., Coffey, Erin E., Laties, Alan M., Rubenstein, Ronald C., Reenstra, William W., Mitchell, Claire H.
Publicado em 2012

Small Heat Shock Protein αA-crystallin Regulates Epithelial Sodium Channel Expression

Por Kashlan, Ossama B., Mueller, Gunhild M., Qamar, Mohammad Z., Poland, Paul A., Ahner, Annette, Rubenstein, Ronald C., Hughey, Rebecca P., Brodsky, Jeffrey L., Kleyman, Thomas R.
Publicado em 2007

Multiple residues in the distal C terminus of the α-subunit have roles in modulating human epithelial sodium channel activity

Por Mueller, Gunhild M., Yan, Wusheng, Copelovitch, Lawrence, Jarman, Susan, Wang, Zhijian, Kinlough, Carol L., Tolino, Michael A., Hughey, Rebecca P., Kleyman, Thomas R., Rubenstein, Ronald C.
Publicado em 2012

Risk Factors for Death of Patients with Cystic Fibrosis Awaiting Lung Transplantation

Por Belkin, Richard A., Henig, Noreen R., Singer, Lianne G., Chaparro, Cecilia, Rubenstein, Ronald C., Xie, Sharon X., Yee, Justin Y., Kotloff, Robert M., Lipson, David A., Bunin, Greta R.
Publicado em 2006

ERp29 Restricts Connexin43 Oligomerization in the Endoplasmic Reticulum

Por Das, Shamie, Smith, Tekla D., Sarma, Jayasri Das, Ritzenthaler, Jeffrey D., Maza, Jose, Kaplan, Benjamin E., Cunningham, Leslie A., Suaud, Laurence, Hubbard, Michael J., Rubenstein, Ronald C., Koval, Michael
Publicado em 2009