Hepatic stress associated with pathologies characterized by disturbed glucose production

door Gjorgjieva, Monika, Mithieux, Gilles, Rajas, Fabienne
Gepubliceerd in Cell Stress (2019)

Glucose-6 Phosphate, a Central Hub for Liver Carbohydrate Metabolism

door Rajas, Fabienne, Gautier-Stein, Amandine, Mithieux, Gilles
Gepubliceerd in Metabolites (2019)

Lessons from new mouse models of glycogen storage disease type 1a in relation to the time course and organ specificity of the disease

door Rajas, Fabienne, clar, julie, Gautier-Stein, Amandine, Mithieux, Gilles
Gepubliceerd in J Inherit Metab Dis (2015)

Glucotoxicity Induces Glucose-6-Phosphatase Catalytic Unit Expression by Acting on the Interaction of HIF-1α With CREB-Binding Protein

door Gautier-Stein, Amandine, Soty, Maud, Chilloux, Julien, Zitoun, Carine, Rajas, Fabienne, Mithieux, Gilles
Gepubliceerd in 2012

Differential regulation of the glucose-6-phosphatase TATA box by intestine-specific homeodomain proteins CDX1 and CDX2

door Gautier-Stein, Amandine, Domon-Dell, Claire, Calon, Alexandre, Bady, Isabelle, Freund, Jean-Noël, Mithieux, Gilles, Rajas, Fabienne
Gepubliceerd in 2003

Targeted deletion of kidney glucose-6 phosphatase leads to nephropathy

door clar, julie, Gri, Blandine, Calderaro, Julien, Birling, Marie-Christine, Herault, Yann, Smith, Peter, Mithieux, Gilles, Rajas, Fabienne
Gepubliceerd in Kidney Int (2014)

In vivo hepatic lipid quantification using MRS at 7 Tesla in a mouse model of glycogen storage disease type 1a

door Ramamonjisoa, Nirilanto, Ratiney, Helene, Mutel, Elodie, Guillou, Herve, Mithieux, Gilles, Pilleul, Frank, Rajas, Fabienne, Beuf, Olivier, Cavassila, Sophie
Gepubliceerd in 2013

Intracellular lipids are an independent cause of liver injury and chronic kidney disease in non alcoholic fatty liver disease-like context

door Monteillet, Laure, Gjorgjieva, Monika, Silva, Marine, Verzieux, Vincent, Imikirene, Linda, Duchampt, Adeline, Guillou, Hervé, Mithieux, Gilles, Rajas, Fabienne
Gepubliceerd in Mol Metab (2018)

G6PC mRNA Therapy Positively Regulates Fasting Blood Glucose and Decreases Liver Abnormalities in a Mouse Model of Glycogen Storage Disease 1a

door Roseman, Daniel S., Khan, Tayeba, Rajas, Fabienne, Jun, Lucy S., Asrani, Kirtika H., Isaacs, Cleo, Farelli, Jeremiah D., Subramanian, Romesh R.
Gepubliceerd in Mol Ther (2018)

The role of kidney in the inter-organ coordination of endogenous glucose production during fasting

door Kaneko, Keizo, Soty, Maud, Zitoun, Carine, Duchampt, Adeline, Silva, Marine, Philippe, Erwann, Gautier-Stein, Amandine, Rajas, Fabienne, Mithieux, Gilles
Gepubliceerd in Mol Metab (2018)

The absence of hepatic glucose-6 phosphatase/ChREBP couple is incompatible with survival in mice

door Rajas, Fabienne, Dentin, Renaud, Cannella Miliano, Alexane, Silva, Marine, Raffin, Margaux, Levavasseur, Françoise, Gautier-Stein, Amandine, Postic, Catherine, Mithieux, Gilles
Gepubliceerd in Mol Metab (2020)

Control of Blood Glucose in the Absence of Hepatic Glucose Production During Prolonged Fasting in Mice: Induction of Renal and Intestinal Gluconeogenesis by Glucagon

door Mutel, Elodie, Gautier-Stein, Amandine, Abdul-Wahed, Aya, Amigó-Correig, Marta, Zitoun, Carine, Stefanutti, Anne, Houberdon, Isabelle, Tourette, Jean-André, Mithieux, Gilles, Rajas, Fabienne
Gepubliceerd in 2011

Glycogen storage disease type 1a is associated with disturbed vitamin A metabolism and elevated serum retinol levels

door Saeed, Ali, Hoogerland, Joanne A, Wessel, Hanna, Heegsma, Janette, Derks, Terry G J, van der Veer, Eveline, Mithieux, Gilles, Rajas, Fabienne, Oosterveer, Maaike H, Faber, Klaas Nico
Gepubliceerd in Hum Mol Genet (2020)

Clinical and biochemical heterogeneity between patients with glycogen storage disease type IA: the added value of CUSUM for metabolic control

door Peeks, Fabian, Steunenberg, Thomas A. H., de Boer, Foekje, Rubio-Gozalbo, M. Estela, Williams, Monique, Burghard, Rob, Rajas, Fabienne, Oosterveer, Maaike H., Weinstein, David A., Derks, Terry G. J.
Gepubliceerd in J Inherit Metab Dis (2017)

A link between hepatic glucose production and peripheral energy metabolism via hepatokines

door Abdul-Wahed, Aya, Gautier-Stein, Amandine, Casteras, Sylvie, Soty, Maud, Roussel, Damien, Romestaing, Caroline, Guillou, Hervé, Tourette, Jean-André, Pleche, Nicolas, Zitoun, Carine, Gri, Blandine, Sardella, Anne, Rajas, Fabienne, Mithieux, Gilles
Gepubliceerd in 2014

Review of the nutritional benefits and risks related to intense sweeteners

door Bruyère, Olivier, Ahmed, Serge H., Atlan, Catherine, Belegaud, Jacques, Bortolotti, Murielle, Canivenc-Lavier, Marie-Chantal, Charrière, Sybil, Girardet, Jean-Philippe, Houdart, Sabine, Kalonji, Esther, Nadaud, Perrine, Rajas, Fabienne, Slama, Gérard, Margaritis, Irène
Gepubliceerd in Arch Public Health (2015)

Erratum to: Review of the nutritional benefits and risks related to intense sweeteners

door Bruyère, Olivier, Ahmed, Serge H., Atlan, Catherine, Belegaud, Jacques, Bortolotti, Murielle, Canivenc-Lavier, Marie-Chantal, Charrière, Sybil, Girardet, Jean-Philippe, Houdart, Sabine, Kalonji, Esther, Nadaud, Perrine, Rajas, Fabienne, Slama, Gérard, Margaritis, Irène
Gepubliceerd in Arch Public Health (2015)

Metabolic Adaptation Establishes Disease Tolerance to Sepsis

door Weis, Sebastian, Carlos, Ana Rita, Moita, Maria Raquel, Singh, Sumnima, Blankenhaus, Birte, Cardoso, Silvia, Larsen, Rasmus, Rebelo, Sofia, Schäuble, Sascha, Del Barrio, Laura, Mithieux, Gilles, Rajas, Fabienne, Lindig, Sandro, Bauer, Michael, Soares, Miguel P.
Gepubliceerd in Cell (2017)

Pathogenesis of Hepatic Tumors following Gene Therapy in Murine and Canine Models of Glycogen Storage Disease

door Kang, Hye-Ri, Gjorgjieva, Monika, Smith, Stephanie N., Brooks, Elizabeth D., Chen, Zelin, Burgess, Shawn M., Chandler, Randy J., Waskowicz, Lauren R., Grady, Kylie M., Li, Songtao, Mithieux, Gilles, Venditti, Charles P., Rajas, Fabienne, Koeberl, Dwight D.
Gepubliceerd in Mol Ther Methods Clin Dev (2019)

Inhibition of Glycogen Synthase II with RNAi Prevents Liver Injury in Mouse Models of Glycogen Storage Diseases

door Pursell, Natalie, Gierut, Jessica, Zhou, Wei, Dills, Michael, Diwanji, Rohan, Gjorgjieva, Monika, Saxena, Utsav, Yang, Jr-Shiuan, Shah, Anee, Venkat, Nandini, Storr, Rachel, Kim, Boyoung, Wang, Weimin, Abrams, Marc, Raffin, Margaux, Mithieux, Gilles, Rajas, Fabienne, Dudek, Henryk, Brown, Bob D., Lai, Chengjung
Gepubliceerd in Mol Ther (2018)