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Establishment and maintenance of an R6/1 transgenic mouse colony and validation of its progressive neurological phenotype to study Huntington’s disease

Huntington’s disease (HD) is a hereditary neurodegenerative disorder of the central nervous system that mainly affects the basal ganglia and has no cure. The mutation is located at an abnormal expansion of the CAG triplet in the Huntingtin gene. Humans show psychiatric, behavioural and motor disorde...

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Dades bibliogràfiques
Publicat a:Veterinaria México
Autors principals: Lucia García-Lara, Adriana Morales-Martínez, Quetzalli D. Angeles-López, Hilda Pedraza-Espitia, Iván Pérez-Neri, Cesar A. Rodríguez-Balderas, Francisca Pérez-Severiano
Format: Artigo
Idioma:Inglês
Publicat: Universidad Nacional Autónoma de México 2018
Matèries:
R6
Accés en línia:https://www.redalyc.org/articulo.oa?id=42371695003
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