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Cystathionine β‐synthase deficiency in the E‐HOD registry‐part I: pyridoxine responsiveness as a determinant of biochemical and clinical phenotype at diagnosis

Cystathionine β‐synthase (CBS) deficiency has a wide clinical spectrum, ranging from neurodevelopmental problems, lens dislocation and marfanoid features in early childhood to adult onset disease with predominantly thromboembolic complications. We have analysed clinical and laboratory data at the ti...

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Detalhes bibliográficos
Publicado no:J Inherit Metab Dis
Main Authors: Kožich, Viktor, Sokolová, Jitka, Morris, Andrew A. M., Pavlíková, Markéta, Gleich, Florian, Kölker, Stefan, Krijt, Jakub, Dionisi‐Vici, Carlo, Baumgartner, Matthias R., Blom, Henk J., Huemer, Martina
Formato: Artigo
Idioma:Inglês
Publicado em: John Wiley & Sons, Inc. 2020
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC8247016/
https://ncbi.nlm.nih.gov/pubmed/33295057
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/jimd.12338
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