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Ultrastructural characterization of peripheral denervation in a mouse model of Type III spinal muscular atrophy

Spinal muscular atrophy (SMA) is a heritable, autosomal recessive neuromuscular disorder characterized by a loss of the survival of motor neurons (SMN) protein, which leads to degeneration of lower motor neurons, and muscle atrophy. Despite SMA being nosographically classified as a motor neuron dise...

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Detalhes bibliográficos
Publicado no:J Neural Transm (Vienna)
Main Authors: Fulceri, Federica, Biagioni, Francesca, Limanaqi, Fiona, Busceti, Carla L., Ryskalin, Larisa, Lenzi, Paola, Fornai, Francesco
Formato: Artigo
Idioma:Inglês
Publicado em: Springer Vienna 2021
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC8205903/
https://ncbi.nlm.nih.gov/pubmed/33999256
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s00702-021-02353-9
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