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Cell-Clearing Systems Bridging Repeat Expansion Proteotoxicity and Neuromuscular Junction Alterations in ALS and SBMA

The coordinated activities of autophagy and the ubiquitin proteasome system (UPS) are key to preventing the aggregation and toxicity of misfold-prone proteins which manifest in a number of neurodegenerative disorders. These include proteins which are encoded by genes containing nucleotide repeat exp...

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Detalhes bibliográficos
Publicado no:Int J Mol Sci
Main Authors: Limanaqi, Fiona, Busceti, Carla Letizia, Biagioni, Francesca, Cantini, Federica, Lenzi, Paola, Fornai, Francesco
Formato: Artigo
Idioma:Inglês
Publicado em: MDPI 2020
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7312203/
https://ncbi.nlm.nih.gov/pubmed/32512809
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms21114021
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