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Cell-Clearing Systems Bridging Repeat Expansion Proteotoxicity and Neuromuscular Junction Alterations in ALS and SBMA

The coordinated activities of autophagy and the ubiquitin proteasome system (UPS) are key to preventing the aggregation and toxicity of misfold-prone proteins which manifest in a number of neurodegenerative disorders. These include proteins which are encoded by genes containing nucleotide repeat exp...

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Autors principals: Fiona Limanaqi, Carla Letizia Busceti, Francesca Biagioni, Federica Cantini, Paola Lenzi, Francesco Fornai
Format: Artigo
Idioma:Inglês
Publicat: MDPI AG 2020-06-01
Col·lecció:International Journal of Molecular Sciences
Matèries:
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Accés en línia:https://www.mdpi.com/1422-0067/21/11/4021
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