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Immune modulation attenuates infantile neuronal ceroid lipofuscinosis in mice before and after disease onset

Targeting neuroinflammation in models for infantile and juvenile forms of neuronal ceroid lipofuscinosis (NCL, CLN disease) with the clinically established immunomodulators fingolimod and teriflunomide significantly attenuates the neurodegenerative phenotype when applied preventively, i.e. before th...

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Detalhes bibliográficos
Publicado no:Brain Commun
Main Authors: Groh, Janos, Berve, Kristina, Martini, Rudolf
Formato: Artigo
Idioma:Inglês
Publicado em: Oxford University Press 2021
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC8098642/
https://ncbi.nlm.nih.gov/pubmed/33977263
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/braincomms/fcab047
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