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Dietary restriction in the long-chain acyl-CoA dehydrogenase knockout mouse

Patients with a disorder of mitochondrial long-chain fatty acid β-oxidation (FAO) have reduced fasting tolerance and may present with hypoketotic hypoglycemia, hepatomegaly, (cardio)myopathy and rhabdomyolysis. Patients should avoid a catabolic state because it increases reliance on FAO as energy so...

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Publicado en:Mol Genet Metab Rep
Main Authors: Diekman, Eugène F., van Weeghel, Michel, Suárez-Fariñas, Mayte, Argmann, Carmen, Ranea-Robles, Pablo, Wanders, Ronald J.A., Visser, Gepke, van der Made, Ingeborg, Creemers, Esther E., Houten, Sander M.
Formato: Artigo
Idioma:Inglês
Publicado: Elsevier 2021
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC8040332/
https://ncbi.nlm.nih.gov/pubmed/33868931
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ymgmr.2021.100749
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