Chargement en cours...

An intellectual disability-associated missense variant in TRMT1 impairs tRNA modification and reconstitution of enzymatic activity

The human TRMT1 gene encodes an RNA methyltransferase enzyme responsible for catalyzing dimethylguanosine (m2,2G) formation in tRNAs. Frameshift mutations in TRMT1 have been shown to cause autosomal-recessive intellectual disability (ID) in the human population but additional TRMT1 variants remain t...

Description complète

Enregistré dans:
Détails bibliographiques
Publié dans:Hum Mutat
Auteurs principaux: Zhang, Kejia, Lentini, Jenna M, Prevost, Christopher T, Hashem, Mais O, Alkuraya, Fowzan S, Fu, Dragony
Format: Artigo
Langue:Inglês
Publié: 2020
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC7981843/
https://ncbi.nlm.nih.gov/pubmed/31898845
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/humu.23976
Tags: Ajouter un tag
Pas de tags, Soyez le premier à ajouter un tag!