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A New Mouse Model Related to SCA14 Carrying a Pseudosubstrate Domain Mutation in PKCγ Shows Perturbed Purkinje Cell Maturation and Ataxic Motor Behavior

Spinocerebellar ataxias (SCAs) are diseases characterized by cerebellar atrophy and loss of Purkinje neurons caused by mutations in diverse genes. In SCA14, the disease is caused by point mutations or small deletions in protein kinase C γ (PKCγ), a crucial signaling protein in Purkinje cells. It is...

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Détails bibliographiques
Publié dans:J Neurosci
Auteurs principaux: Shimobayashi, Etsuko, Kapfhammer, Josef P.
Format: Artigo
Langue:Inglês
Publié: Society for Neuroscience 2021
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC7939089/
https://ncbi.nlm.nih.gov/pubmed/33478986
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1523/JNEUROSCI.1946-20.2021
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