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The Newborn Fmr1 Knockout Mouse: A Novel Model of Excess Ubiquinone and Closed Mitochondrial Permeability Transition Pore in the Developing Heart

BACKGROUND: Mitochondrial permeability transition pore (mPTP) closure triggers cardiomyocyte differentiation during development while pathological opening causes cell death during myocardial ischemia-reperfusion and heart failure. Ubiquinone modulates the mPTP, however, little is known about its mec...

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Detalhes bibliográficos
Publicado no:Pediatr Res
Main Authors: Barajas, Matthew, Wang, Aili, Griffiths, Keren K., Matsumoto, Kenji, Liu, Rui, Homma, Shunichi, Levy, Richard J.
Formato: Artigo
Idioma:Inglês
Publicado em: 2020
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7855053/
https://ncbi.nlm.nih.gov/pubmed/32674111
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41390-020-1064-6
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