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DNA ligase I variants fail in the ligation of mutagenic repair intermediates with mismatches and oxidative DNA damage

DNA ligase I (LIG1) joins DNA strand breaks during DNA replication and repair transactions and contributes to genome integrity. The mutations (P529L, E566K, R641L and R771W) in LIG1 gene are described in patients with LIG1-deficiency syndrome that exhibit immunodeficiency. LIG1 senses 3’-DNA ends wi...

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Bibliografske podrobnosti
izdano v:Mutagenesis
Main Authors: Tang, Qun, Kamble, Pradnya, Çağlayan, Melike
Format: Artigo
Jezik:Inglês
Izdano: Oxford University Press 2020
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC7846189/
https://ncbi.nlm.nih.gov/pubmed/32914844
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/mutage/geaa023
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