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DNA ligase I variants fail in the ligation of mutagenic repair intermediates with mismatches and oxidative DNA damage

DNA ligase I (LIG1) joins DNA strand breaks during DNA replication and repair transactions and contributes to genome integrity. The mutations (P529L, E566K, R641L and R771W) in LIG1 gene are described in patients with LIG1-deficiency syndrome that exhibit immunodeficiency. LIG1 senses 3’-DNA ends wi...

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Detalhes bibliográficos
Publicado no:Mutagenesis
Principais autores: Tang, Qun, Kamble, Pradnya, Çağlayan, Melike
Formato: Artigo
Idioma:Inglês
Publicado em: Oxford University Press 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7846189/
https://ncbi.nlm.nih.gov/pubmed/32914844
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/mutage/geaa023
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