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trans-3-methylglutaconyl CoA isomerization-dependent protein acylation

3-methylglutaconic (3MGC) aciduria is associated with a growing number of discrete inborn errors of metabolism. Herein, an antibody-based approach to detection / quantitation of 3MGC acid has been pursued. When trans-3MGC acid conjugated keyhole limpet hemocyanin (KLH) was inoculated into rabbits a...

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Pubblicato in:Biochem Biophys Res Commun
Autori principali: Young, Rebecca, Jones, Dylan E., Diacovich, Lautaro, Witkowski, Andrzej, Ryan, Robert O.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2020
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7785636/
https://ncbi.nlm.nih.gov/pubmed/33280817
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.bbrc.2020.11.100
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