Chargement en cours...

Late‐Onset Tay‐Sachs Disease in an Irish Family

BACKGROUND: Late‐onset Tay‐Sachs disease (LOTS) is an autosomal‐recessive lysosomal storage disease caused by deficient β‐hexosaminidase A activity. LOTS is rare in the Ashkenazi Jews, but even rarer in the non‐Jewish population. CASES: We report an Irish family expanding the LOTS phenotype (ataxia,...

Description complète

Enregistré dans:
Détails bibliographiques
Publié dans:Mov Disord Clin Pract
Auteurs principaux: Lefter, Stela, O' Mahony, Olivia, Sweeney, Brian, Ryan, Aisling M.
Format: Artigo
Langue:Inglês
Publié: John Wiley & Sons, Inc. 2020
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC7780940/
https://ncbi.nlm.nih.gov/pubmed/33426165
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/mdc3.13096
Tags: Ajouter un tag
Pas de tags, Soyez le premier à ajouter un tag!