טוען...

Biotinidase deficiency is a rare, potentially treatable cause of peripheral neuropathy with or without optic neuropathy in adults

BACKGROUND: We describe two adult brothers with lower limb neuropathy and one with progressive optic neuropathy. One brother was found to have profound biotinidase deficiency by identifying biallelic pathogenic variants of the BTD gene by whole exome sequencing, which was confirmed by markedly decre...

תיאור מלא

שמור ב:
מידע ביבליוגרפי
הוצא לאור ב:Mol Genet Metab Rep
Main Authors: Kellom, Elizabeth, Stepien, Kimberly, Rice, Gregory, Wolf, Barry
פורמט: Artigo
שפה:Inglês
יצא לאור: Elsevier 2020
נושאים:
גישה מקוונת:https://ncbi.nlm.nih.gov/pmc/articles/PMC7750409/
https://ncbi.nlm.nih.gov/pubmed/33364171
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ymgmr.2020.100696
תגים: הוספת תג
אין תגיות, היה/י הראשונ/ה לתייג את הרשומה!