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Biotinidase deficiency is a rare, potentially treatable cause of peripheral neuropathy with or without optic neuropathy in adults

BACKGROUND: We describe two adult brothers with lower limb neuropathy and one with progressive optic neuropathy. One brother was found to have profound biotinidase deficiency by identifying biallelic pathogenic variants of the BTD gene by whole exome sequencing, which was confirmed by markedly decre...

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Détails bibliographiques
Publié dans:Mol Genet Metab Rep
Auteurs principaux: Kellom, Elizabeth, Stepien, Kimberly, Rice, Gregory, Wolf, Barry
Format: Artigo
Langue:Inglês
Publié: Elsevier 2020
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC7750409/
https://ncbi.nlm.nih.gov/pubmed/33364171
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ymgmr.2020.100696
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