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Molecular Mechanisms Underlying Muscle Wasting in Huntington’s Disease

Huntington’s disease (HD) is an autosomal dominant neurodegenerative disorder caused by pathogenic expansions of the triplet cytosine-adenosine-guanosine (CAG) within the Huntingtin gene. These expansions lead to a prolongation of the poly-glutamine stretch at the N-terminus of Huntingtin causing pr...

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Dades bibliogràfiques
Publicat a:Int J Mol Sci
Autors principals: Bozzi, Manuela, Sciandra, Francesca
Format: Artigo
Idioma:Inglês
Publicat: MDPI 2020
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7664236/
https://ncbi.nlm.nih.gov/pubmed/33167595
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms21218314
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