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Vasculitis as a Major Morbidity Factor in Patients With Partial RAG Deficiency

Vasculitis can be a life-threatening complication associated with high mortality and morbidity among patients with primary immunodeficiencies (PIDs), including variants of severe and combined immunodeficiencies ((S)CID). Our understanding of vasculitis in partial defects in recombination activating...

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Bibliografiset tiedot
Julkaisussa:Front Immunol
Päätekijät: Geier, Christoph B., Farmer, Jocelyn R., Foldvari, Zsofia, Ujhazi, Boglarka, Steininger, Jolanda, Sleasman, John W., Parikh, Suhag, Dilley, Meredith A., Pai, Sung-Yun, Henderson, Lauren, Hazen, Melissa, Neven, Benedicte, Moshous, Despina, Sharapova, Svetlana O., Mihailova, Snezhina, Yankova, Petya, Naumova, Elisaveta, Özen, Seza, Byram, Kevin, Fernandez, James, Wolf, Hermann M., Eibl, Martha M., Notarangelo, Luigi D., Calabrese, Leonard H., Walter, Jolan E.
Aineistotyyppi: Artigo
Kieli:Inglês
Julkaistu: Frontiers Media S.A. 2020
Aiheet:
Linkit:https://ncbi.nlm.nih.gov/pmc/articles/PMC7609967/
https://ncbi.nlm.nih.gov/pubmed/33193364
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fimmu.2020.574738
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