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Vasculitis as a Major Morbidity Factor in Patients With Partial RAG Deficiency

Vasculitis can be a life-threatening complication associated with high mortality and morbidity among patients with primary immunodeficiencies (PIDs), including variants of severe and combined immunodeficiencies ((S)CID). Our understanding of vasculitis in partial defects in recombination activating...

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Detalhes bibliográficos
Publicado no:Front Immunol
Main Authors: Geier, Christoph B., Farmer, Jocelyn R., Foldvari, Zsofia, Ujhazi, Boglarka, Steininger, Jolanda, Sleasman, John W., Parikh, Suhag, Dilley, Meredith A., Pai, Sung-Yun, Henderson, Lauren, Hazen, Melissa, Neven, Benedicte, Moshous, Despina, Sharapova, Svetlana O., Mihailova, Snezhina, Yankova, Petya, Naumova, Elisaveta, Özen, Seza, Byram, Kevin, Fernandez, James, Wolf, Hermann M., Eibl, Martha M., Notarangelo, Luigi D., Calabrese, Leonard H., Walter, Jolan E.
Formato: Artigo
Idioma:Inglês
Publicado em: Frontiers Media S.A. 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7609967/
https://ncbi.nlm.nih.gov/pubmed/33193364
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fimmu.2020.574738
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