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Genetic compensation prevents myopathy and heart failure in an in vivo model of Bag3 deficiency

Mutations in the molecular co-chaperone Bcl2-associated athanogene 3 (BAG3) are found to cause dilated cardiomyopathy (DCM), resulting in systolic dysfunction and heart failure, as well as myofibrillar myopathy (MFM), which is characterized by protein aggregation and myofibrillar disintegration in s...

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Detalhes bibliográficos
Publicado no:PLoS Genet
Main Authors: Diofano, Federica, Weinmann, Karolina, Schneider, Isabelle, Thiessen, Kevin D., Rottbauer, Wolfgang, Just, Steffen
Formato: Artigo
Idioma:Inglês
Publicado em: Public Library of Science 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7605898/
https://ncbi.nlm.nih.gov/pubmed/33137814
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pgen.1009088
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