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Dysregulated signalling pathways in innate immune cells with cystic fibrosis mutations

Cystic fibrosis (CF) is one of the most common life-limiting recessive genetic disorders in Caucasians, caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR). CF is a multi-organ disease that involves the lungs, pancreas, sweat glands, digestive and reproductive syste...

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Détails bibliographiques
Publié dans:Cell Mol Life Sci
Auteurs principaux: Lara-Reyna, Samuel, Holbrook, Jonathan, Jarosz-Griffiths, Heledd H., Peckham, Daniel, McDermott, Michael F.
Format: Artigo
Langue:Inglês
Publié: Springer International Publishing 2020
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC7599191/
https://ncbi.nlm.nih.gov/pubmed/32367193
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s00018-020-03540-9
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