Caricamento...

Diphthamide-deficiency syndrome: a novel human developmental disorder and ribosomopathy

We describe a novel type of ribosomopathy that is defined by deficiency in diphthamidylation of translation elongation factor 2. The ribosomopathy was identified by correlating phenotypes and biochemical properties of previously described patients with diphthamide biosynthesis gene 1 (DPH1) deficien...

Descrizione completa

Salvato in:
Dettagli Bibliografici
Pubblicato in:Eur J Hum Genet
Autori principali: Hawer, Harmen, Mendelsohn, Bryce A., Mayer, Klaus, Kung, Ann, Malhotra, Amit, Tuupanen, Sari, Schleit, Jennifer, Brinkmann, Ulrich, Schaffrath, Raffael
Natura: Artigo
Lingua:Inglês
Pubblicazione: Springer International Publishing 2020
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7575589/
https://ncbi.nlm.nih.gov/pubmed/32576952
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41431-020-0668-y
Tags: Aggiungi Tag
Nessun Tag, puoi essere il primo ad aggiungerne! !