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Cystic Fibrosis Transmembrane Conductance Regulator Modulator Therapy: A Review for the Otolaryngologist

BACKGROUND: Cystic fibrosis (CF) is a genetic disease that may result in multiple systemic disorders and potentially fatal severe respiratory compromise. However, the advent of CF transmembrane conductance regulator (CFTR) modulators has changed the management of CF for patients with select mutation...

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Detalles Bibliográficos
Publicado en:Am J Rhinol Allergy
Main Authors: Lee, Saangyoung E., Farzal, Zainab, Daniels, M.Leigh Anne, Thorp, Brian D., Zanation, Adam M., Senior, Brent A., Ebert, Charles S., Kimple, Adam J.
Formato: Artigo
Idioma:Inglês
Publicado: SAGE Publications 2020
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC7573678/
https://ncbi.nlm.nih.gov/pubmed/32168995
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1177/1945892420912368
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