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Cystic Fibrosis Transmembrane Conductance Regulator Modulator Therapy: A Review for the Otolaryngologist

BACKGROUND: Cystic fibrosis (CF) is a genetic disease that may result in multiple systemic disorders and potentially fatal severe respiratory compromise. However, the advent of CF transmembrane conductance regulator (CFTR) modulators has changed the management of CF for patients with select mutation...

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Dades bibliogràfiques
Publicat a:Am J Rhinol Allergy
Autors principals: Lee, Saangyoung E., Farzal, Zainab, Daniels, M.Leigh Anne, Thorp, Brian D., Zanation, Adam M., Senior, Brent A., Ebert, Charles S., Kimple, Adam J.
Format: Artigo
Idioma:Inglês
Publicat: SAGE Publications 2020
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7573678/
https://ncbi.nlm.nih.gov/pubmed/32168995
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1177/1945892420912368
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