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Interleukin-1 Receptor-Associated Kinase 4 Deficiency in a Greek Teenager

BACKGROUND: Human interleukin- (IL-) 1 receptor-associated kinase 4 (IRAK-4) deficiency is a recently described primary immunodeficiency. It is a rare, autosomal recessive immunodeficiency that impairs toll/IL-1R immunity, except for the toll-like receptor (TLR) 3- and TLR4-interferon alpha (IFNA)/b...

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Détails bibliographiques
Publié dans:Case Reports Immunol
Auteurs principaux: Karananou, Panagiota, Alataki, Anastasia, Papadopoulou-Alataki, Efimia
Format: Artigo
Langue:Inglês
Publié: Hindawi 2020
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC7568159/
https://ncbi.nlm.nih.gov/pubmed/33101742
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2020/8846827
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