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Interleukin-1 Receptor-Associated Kinase 4 Deficiency in a Greek Teenager
BACKGROUND: Human interleukin- (IL-) 1 receptor-associated kinase 4 (IRAK-4) deficiency is a recently described primary immunodeficiency. It is a rare, autosomal recessive immunodeficiency that impairs toll/IL-1R immunity, except for the toll-like receptor (TLR) 3- and TLR4-interferon alpha (IFNA)/b...
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| Publicado no: | Case Reports Immunol |
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| Main Authors: | , , |
| Formato: | Artigo |
| Idioma: | Inglês |
| Publicado em: |
Hindawi
2020
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| Assuntos: | |
| Acesso em linha: | https://ncbi.nlm.nih.gov/pmc/articles/PMC7568159/ https://ncbi.nlm.nih.gov/pubmed/33101742 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2020/8846827 |
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