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Anesthesia management in a patient with very long-chain acyl-Coenzyme A dehydrogenase deficiency

BACKGROUND: In a patient with very long-chain acyl-Coenzyme A dehydrogenase (VLCAD) deficiency, metabolism of fatty acids is impaired and a supply of alternative energy is limited when glucose level is insufficient on starvation. CASE PRESENTATION: A 37-year-old woman with VLCAD deficiency was diagn...

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Publicado en:JA Clin Rep
Main Authors: Yuasa, Haruyuki, Onoda, Yukio, Kitaura, Atsuhiro, Mino, Takashi, Tsukimoto, Shota, Nakao, Shinichi
Formato: Artigo
Idioma:Inglês
Publicado: Springer Berlin Heidelberg 2020
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC7494713/
https://ncbi.nlm.nih.gov/pubmed/32939699
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s40981-020-00379-8
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