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Very Long-Chain Acyl-Coenzyme A Dehydrogenase Deficiency and Perioperative Management in Adult Patients

Surgery and anesthesia pose a threat to patients with very long-chain acyl-CoA dehydrogenase deficiency (VLCADD), because prolonged fasting, stress, and pain are known risk factors for the induction of metabolic derangement. The optimal perioperative management in these patients is unknown and the u...

Ausführliche Beschreibung

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Bibliographische Detailangaben
Veröffentlicht in:JIMD Rep
Hauptverfasser: Welsink-Karssies, M. M., Polderman, J. A. W., Nieveen van Dijkum, E. J., Preckel, B., Schlack, W. S., Visser, G., Hollak, C. E., Hermanides, J.
Format: Artigo
Sprache:Inglês
Veröffentlicht: Springer Berlin Heidelberg 2016
Schlagworte:
Online Zugang:https://ncbi.nlm.nih.gov/pmc/articles/PMC5509551/
https://ncbi.nlm.nih.gov/pubmed/27518779
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/8904_2016_6
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