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Lipid and energy metabolism in Wilson disease()

Copper accumulation and deficiency are reciprocally connected to lipid metabolism. In Wilson disease (WD), which is caused by a genetic loss of function of the copper-transporting P-type ATPase beta, copper accumulates mainly in the liver and lipid metabolism is dysregulated. The underlying mechanis...

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Publicado en:Liver Res
Autores principales: Mazi, Tagreed A., Shibata, Noreene M., Medici, Valentina
Formato: Artigo
Lenguaje:Inglês
Publicado: 2020
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC7437987/
https://ncbi.nlm.nih.gov/pubmed/32832193
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.livres.2020.02.002
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