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Dysregulated Choline, Methionine, and Aromatic Amino Acid Metabolism in Patients with Wilson Disease: Exploratory Metabolomic Profiling and Implications for Hepatic and Neurologic Phenotypes

Wilson disease (WD) is a genetic copper overload condition characterized by hepatic and neuropsychiatric symptoms with a not well-understood pathogenesis. Dysregulated methionine cycle is reported in animal models of WD, though not verified in humans. Choline is essential for lipid and methionine me...

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Bibliografiske detaljer
Udgivet i:Int J Mol Sci
Main Authors: Mazi, Tagreed A., Sarode, Gaurav V., Czlonkowska, Anna, Litwin, Tomasz, Kim, Kyoungmi, Shibata, Noreene M., Medici, Valentina
Format: Artigo
Sprog:Inglês
Udgivet: MDPI 2019
Fag:
Online adgang:https://ncbi.nlm.nih.gov/pmc/articles/PMC6928853/
https://ncbi.nlm.nih.gov/pubmed/31779102
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms20235937
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