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Stochastic allelic expression as trigger for contractile imbalance in hypertrophic cardiomyopathy

Hypertrophic cardiomyopathy (HCM), the most common inherited cardiac disease, is caused by several mostly heterozygous mutations in sarcomeric genes. Hallmarks of HCM are cardiomyocyte and myofibrillar disarray and hypertrophy and fibrosis of the septum and the left ventricle. To date, a pathomechan...

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Dades bibliogràfiques
Publicat a:Biophys Rev
Autors principals: Montag, Judith, Kraft, Theresia
Format: Artigo
Idioma:Inglês
Publicat: Springer Berlin Heidelberg 2020
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7429642/
https://ncbi.nlm.nih.gov/pubmed/32661905
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s12551-020-00719-z
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