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Transgenic animal models of congenital diaphragmatic hernia: a comprehensive overview of candidate genes and signaling pathways

Congenital diaphragmatic hernia (CDH) is a relatively common and life-threatening birth defect, characterized by incomplete formation of the diaphragm. Because CDH herniation occurs at the same time as preacinar airway branching, normal lung development becomes severely disrupted, resulting almost i...

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Publicat a:Pediatr Surg Int
Autors principals: Nakamura, Hiroki, Doi, Takashi, Puri, Prem, Friedmacher, Florian
Format: Artigo
Idioma:Inglês
Publicat: Springer Berlin Heidelberg 2020
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7385019/
https://ncbi.nlm.nih.gov/pubmed/32591848
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s00383-020-04705-0
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