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Transgenic animal models of congenital diaphragmatic hernia: a comprehensive overview of candidate genes and signaling pathways

Congenital diaphragmatic hernia (CDH) is a relatively common and life-threatening birth defect, characterized by incomplete formation of the diaphragm. Because CDH herniation occurs at the same time as preacinar airway branching, normal lung development becomes severely disrupted, resulting almost i...

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Detalhes bibliográficos
Publicado no:Pediatr Surg Int
Main Authors: Nakamura, Hiroki, Doi, Takashi, Puri, Prem, Friedmacher, Florian
Formato: Artigo
Idioma:Inglês
Publicado em: Springer Berlin Heidelberg 2020
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7385019/
https://ncbi.nlm.nih.gov/pubmed/32591848
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s00383-020-04705-0
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