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Intrinsic Abnormalities of Cystic Fibrosis Airway Connective Tissue Revealed by an In Vitro 3D Stromal Model

Cystic fibrosis is characterized by lung dysfunction involving mucus hypersecretion, bacterial infections, and inflammatory response. Inflammation triggers pro-fibrotic signals that compromise lung structure and function. At present, several in vitro cystic fibrosis models have been developed to stu...

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Dettagli Bibliografici
Pubblicato in:Cells
Autori principali: Mazio, Claudia, Scognamiglio, Laura S., De Cegli, Rossella, Galietta, Luis J. V., Di Bernardo, Diego, Casale, Costantino, Urciuolo, Francesco, Imparato, Giorgia, Netti, Paolo A.
Natura: Artigo
Lingua:Inglês
Pubblicazione: MDPI 2020
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7348935/
https://ncbi.nlm.nih.gov/pubmed/32492951
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/cells9061371
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