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Abnormal localization of cystic fibrosis transmembrane conductance regulator in primary cultures of cystic fibrosis airway epithelia

Cystic fibrosis (CF) is caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR), a membrane glycoprotein that forms Cl- channels. Previous work has shown that when some CF- associated mutants of CFTR are expressed in heterologous cells, their glycosylation is incomplete...

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Detalles Bibliográficos
Formato: Artigo
Lenguaje:Inglês
Publicado: The Rockefeller University Press 1992
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2289545/
https://ncbi.nlm.nih.gov/pubmed/1379244
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