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Cholesterol Transport in Wild-Type NPC1 and P691S: Molecular Dynamics Simulations Reveal Changes in Dynamical Behavior

The Niemann–Pick C1 (NPC1) protein is the main protein involved in NPC disease, a fatal lysosomal lipid storage disease. NPC1, containing 1278 amino acids, is comprised of three lumenal domains (N-terminal, middle lumenal, C-terminal) and a transmembrane (TM) domain that contains a five helix bundle...

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Bibliografski detalji
Izdano u:Int J Mol Sci
Glavni autor: Elghobashi-Meinhardt, Nadia
Format: Artigo
Jezik:Inglês
Izdano: MDPI 2020
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC7215871/
https://ncbi.nlm.nih.gov/pubmed/32331453
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms21082962
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