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Clinical Spectrum of KCNA1 Mutations: New Insights into Episodic Ataxia and Epilepsy Comorbidity

Mutations in the KCNA1 gene, which encodes voltage-gated Kv1.1 potassium channel α-subunits, cause a variety of human diseases, complicating simple genotype–phenotype correlations in patients. KCNA1 mutations are primarily associated with a rare neurological movement disorder known as episodic ataxi...

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Detalhes bibliográficos
Publicado no:Int J Mol Sci
Main Authors: Paulhus, Kelsey, Ammerman, Lauren, Glasscock, Edward
Formato: Artigo
Idioma:Inglês
Publicado em: MDPI 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7215408/
https://ncbi.nlm.nih.gov/pubmed/32316562
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms21082802
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