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MON-218 Clinical and Genetic Aspects of Pediatric Pheochromocytomas and Paragangliomas

Pheochromocytomas and paragangliomas (PPGLs) are neuroendocrine tumors derived from chromaffin cells. At least 30% of PPGL patients have hereditary predisposition. PPGLs in children are more often hereditary, multiple and extra-adrenal. To date, more than 14 tumor-susceptibility genes have been repo...

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Wedi'i Gadw mewn:
Manylion Llyfryddiaeth
Cyhoeddwyd yn:J Endocr Soc
Prif Awduron: Petenuci, Janaina, Guimaraes, Augusto, Benedetti, Anna Flavia Figueredo, Fagundes, Gustavo Freitas Cardoso, Pereira, Maria Adelaide, D’Eur, Joya Emilie Correa, Zerbini, Maria Claudia, Siqueira, Sheila, Yamauchi, Fernando, Soares, Silvia, Srougi, Vitor, Tanno, Fabio Y, Chambo, Jose L, Denes, Francisco T, Hoff, Ana O, Latronico, Ana Claudia, Mendonca, Berenice Bilharinho, Fragoso, Maria Candida B V, Almeida, Madson Q
Fformat: Artigo
Iaith:Inglês
Cyhoeddwyd: Oxford University Press 2020
Pynciau:
Mynediad Ar-lein:https://ncbi.nlm.nih.gov/pmc/articles/PMC7208869/
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1210/jendso/bvaa046.816
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