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MON-218 Clinical and Genetic Aspects of Pediatric Pheochromocytomas and Paragangliomas

Pheochromocytomas and paragangliomas (PPGLs) are neuroendocrine tumors derived from chromaffin cells. At least 30% of PPGL patients have hereditary predisposition. PPGLs in children are more often hereditary, multiple and extra-adrenal. To date, more than 14 tumor-susceptibility genes have been repo...

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Detalhes bibliográficos
Publicado no:J Endocr Soc
Main Authors: Petenuci, Janaina, Guimaraes, Augusto, Benedetti, Anna Flavia Figueredo, Fagundes, Gustavo Freitas Cardoso, Pereira, Maria Adelaide, D’Eur, Joya Emilie Correa, Zerbini, Maria Claudia, Siqueira, Sheila, Yamauchi, Fernando, Soares, Silvia, Srougi, Vitor, Tanno, Fabio Y, Chambo, Jose L, Denes, Francisco T, Hoff, Ana O, Latronico, Ana Claudia, Mendonca, Berenice Bilharinho, Fragoso, Maria Candida B V, Almeida, Madson Q
Formato: Artigo
Idioma:Inglês
Publicado em: Oxford University Press 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7208869/
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1210/jendso/bvaa046.816
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