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SUN-218 Analysis of ATRX and ZNRF3 Expression and Copy Number Variation in a Pediatric and Adult Cohort with Adrenocortical Tumors

Introduction: Adrenocortical carcinoma (ACC) is a rare malignancy with an incidence of 1 to 2 cases per million/year in adults and with a global survival rate of less than 40% in 5 years. ACC diagnosis was based on Weiss criteria for adult patients. Pediatric patients with adrenocortical tumors (PAT...

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Vydáno v:J Endocr Soc
Hlavní autoři: Brondani, Vânia Balderrama, Montenegro, Luciana Ribeiro, Mariani, Beatriz Marinho, Nishi, Mirian Yumie, Zerbini, Maria Claudia N, Lacombe, Amanda Meneses Ferreira, Tanno, Fabio Y, Srougi, Victor, Chambo, Jose L, Denes, Francisco T, Mendonca, Berenice B, Almeida, Madson Q, Villares Fragoso, Maria Candida Barisson
Médium: Artigo
Jazyk:Inglês
Vydáno: Oxford University Press 2020
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On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC7207917/
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1210/jendso/bvaa046.1190
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