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Slc22a5 haploinsufficiency does not aggravate the phenotype of the long-chain acyl-CoA dehydrogenase KO mouse

Secondary carnitine deficiency is commonly observed in inherited metabolic diseases characterized by the accumulation of acylcarnitines such as mitochondrial fatty acid oxidation (FAO) disorders. It is currently unclear if carnitine deficiency and/or acylcarnitine accumulation play a role in the pat...

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Détails bibliographiques
Publié dans:J Inherit Metab Dis
Auteurs principaux: Ranea-Robles, Pablo, Yu, Chunli, van Vlies, Naomi, Vaz, Frédéric M., Houten, Sander M.
Format: Artigo
Langue:Inglês
Publié: 2019
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC7205564/
https://ncbi.nlm.nih.gov/pubmed/31845336
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/jimd.12204
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