Caricamento...

Slc22a5 haploinsufficiency does not aggravate the phenotype of the long-chain acyl-CoA dehydrogenase KO mouse

Secondary carnitine deficiency is commonly observed in inherited metabolic diseases characterized by the accumulation of acylcarnitines such as mitochondrial fatty acid oxidation (FAO) disorders. It is currently unclear if carnitine deficiency and/or acylcarnitine accumulation play a role in the pat...

Descrizione completa

Salvato in:
Dettagli Bibliografici
Pubblicato in:J Inherit Metab Dis
Autori principali: Ranea-Robles, Pablo, Yu, Chunli, van Vlies, Naomi, Vaz, Frédéric M., Houten, Sander M.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2019
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7205564/
https://ncbi.nlm.nih.gov/pubmed/31845336
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/jimd.12204
Tags: Aggiungi Tag
Nessun Tag, puoi essere il primo ad aggiungerne! !