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Systematic misclassification of missense variants in BRCA1 and BRCA2 “coldspots”

PURPOSE: Guidelines for variant interpretation incorporate variant hotspots in critical functional domains as evidence for pathogenicity (e.g., PM1 and PP2), but do not use “coldspots,” that is, regions without essential functions that tolerate variation, as evidence a variant is benign. To improve...

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Publicat a:Genet Med
Autors principals: Dines, Jennifer N., Shirts, Brian H., Slavin, Thomas P., Walsh, Tom, King, Mary-Claire, Fowler, Douglas M., Pritchard, Colin C.
Format: Artigo
Idioma:Inglês
Publicat: Nature Publishing Group US 2020
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7200594/
https://ncbi.nlm.nih.gov/pubmed/31911673
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41436-019-0740-6
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