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Expression of interferon-regulated genes in juvenile dermatomyositis versus Mendelian autoinflammatory interferonopathies

BACKGROUND: Juvenile dermatomyositis (JDM) is a systemic autoimmune disease with a prominent interferon (IFN) signature, but the pathogenesis of JDM and the etiology of its IFN signature remain unknown. The Mendelian autoinflammatory interferonopathies, Chronic Atypical Neutrophilic Dermatosis with...

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Detalhes bibliográficos
Publicado no:Arthritis Res Ther
Main Authors: Kim, Hanna, Gunter-Rahman, Fatima, McGrath, John A., Lee, Esther, de Jesus, Adriana A., Targoff, Ira N., Huang, Yan, O’Hanlon, Terrance P., Tsai, Wanxia L., Gadina, Massimo, Miller, Frederick W., Goldbach-Mansky, Raphaela, Rider, Lisa G.
Formato: Artigo
Idioma:Inglês
Publicado em: BioMed Central 2020
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7137415/
https://ncbi.nlm.nih.gov/pubmed/32252809
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13075-020-02160-9
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