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Insights from Mendelian Interferonopathies: Comparison of CANDLE, SAVI with AGS, Monogenic Lupus

Autoinflammatory disorders are sterile inflammatory conditions characterized by episodes of early-onset fever and disease-specific patterns of organ inflammation. Recently, the discoveries of monogenic disorders with strong type I interferon (IFN) signatures caused by mutations in proteasome degrada...

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Bibliografske podrobnosti
izdano v:J Mol Med (Berl)
Main Authors: Kim, Hanna, Montealegre Sanchez, Gina A., Goldbach-Mansky, Raphaela
Format: Artigo
Jezik:Inglês
Izdano: 2016
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC5094849/
https://ncbi.nlm.nih.gov/pubmed/27678529
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s00109-016-1465-5
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