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Abnormally increased carotid intima media-thickness and elasticity in patients with Morquio A disease

BACKGROUND: Cardiovascular disease frequently causes morbidity and mortality in mucopolysaccharidoses (MPS); however, cardiovascular anatomy and dysfunction in MPS IVA (Morquio A disease) is not well described. Consequently, the study aimed to compare carotid artery structure and elasticity of MPS I...

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Détails bibliographiques
Publié dans:Orphanet J Rare Dis
Auteurs principaux: Wang, Raymond Y., Rudser, Kyle D., Dengel, Donald R., Evanoff, Nicholas, Steinberger, Julia, Movsesyan, Nina, Garrett, Robert, Christensen, Katherine, Boylan, Deborah, Braddock, Stephen R., Shinawi, Marwan, Gan, Qi, Montaño, Adriana M.
Format: Artigo
Langue:Inglês
Publié: BioMed Central 2020
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC7079365/
https://ncbi.nlm.nih.gov/pubmed/32183856
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-020-1331-y
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