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Abnormally increased carotid intima media-thickness and elasticity in patients with Morquio A disease

BACKGROUND: Cardiovascular disease frequently causes morbidity and mortality in mucopolysaccharidoses (MPS); however, cardiovascular anatomy and dysfunction in MPS IVA (Morquio A disease) is not well described. Consequently, the study aimed to compare carotid artery structure and elasticity of MPS I...

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Pubblicato in:Orphanet J Rare Dis
Autori principali: Wang, Raymond Y., Rudser, Kyle D., Dengel, Donald R., Evanoff, Nicholas, Steinberger, Julia, Movsesyan, Nina, Garrett, Robert, Christensen, Katherine, Boylan, Deborah, Braddock, Stephen R., Shinawi, Marwan, Gan, Qi, Montaño, Adriana M.
Natura: Artigo
Lingua:Inglês
Pubblicazione: BioMed Central 2020
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7079365/
https://ncbi.nlm.nih.gov/pubmed/32183856
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-020-1331-y
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