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Abnormally increased carotid intima media-thickness and elasticity in patients with Morquio A disease

BACKGROUND: Cardiovascular disease frequently causes morbidity and mortality in mucopolysaccharidoses (MPS); however, cardiovascular anatomy and dysfunction in MPS IVA (Morquio A disease) is not well described. Consequently, the study aimed to compare carotid artery structure and elasticity of MPS I...

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Detalles Bibliográficos
Publicado en:Orphanet J Rare Dis
Main Authors: Wang, Raymond Y., Rudser, Kyle D., Dengel, Donald R., Evanoff, Nicholas, Steinberger, Julia, Movsesyan, Nina, Garrett, Robert, Christensen, Katherine, Boylan, Deborah, Braddock, Stephen R., Shinawi, Marwan, Gan, Qi, Montaño, Adriana M.
Formato: Artigo
Idioma:Inglês
Publicado: BioMed Central 2020
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC7079365/
https://ncbi.nlm.nih.gov/pubmed/32183856
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-020-1331-y
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