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Small Molecule Anion Carriers Correct Abnormal Airway Surface Liquid Properties in Cystic Fibrosis Airway Epithelia

Cystic fibrosis (CF) is a genetic disease characterized by the lack of cystic fibrosis transmembrane conductance regulator (CFTR) protein expressed in epithelial cells. The resulting defective chloride and bicarbonate secretion and imbalance of the transepithelial homeostasis lead to abnormal airway...

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Detalhes bibliográficos
Publicado no:Int J Mol Sci
Main Authors: Gianotti, Ambra, Capurro, Valeria, Delpiano, Livia, Mielczarek, Marcin, García-Valverde, María, Carreira-Barral, Israel, Ludovico, Alessandra, Fiore, Michele, Baroni, Debora, Moran, Oscar, Quesada, Roberto, Caci, Emanuela
Formato: Artigo
Idioma:Inglês
Publicado em: MDPI 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7073096/
https://ncbi.nlm.nih.gov/pubmed/32098269
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms21041488
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